Type I IFN-related NETosis in ataxia telangiectasia and Artemis deficiency

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2018-07-01
Gul, Ersin
Sayar, Esra Hazar
Gungor, Bilgi
Eroglu, Fehime Kara
Surucu, Naz
Keleş, Sevgi
Güner, Şükrü Nail
Findik, Siddika
Alpdundar, Esin
Ayanoğlu, İhsan Cihan
Kayaoğlu, Başak
Geckin, Busra Nur
Sanli, Hatice Asena
Kahraman, Tamer
Yakicier, Cengiz
Müftüoğlu, Meltem
Oğuz, Berna
Çağdaş Ayvaz, Deniz Nazire
Gürsel, İhsan
Özen, Seza
Reisli, İsmail
Gürsel, Mayda
Background: Pathological inflammatory syndromes of unknown etiology are commonly observed in ataxia telangiectasia (AT) and Artemis deficiency. Similar inflammatory manifestations also exist in patients with STING-associated vasculopathy in infancy (SAVI).